Congenital occlusion of ureterovesical orifice

This code describes a birth defect where the opening between the ureter and the bladder is blocked or narrowed. This obstruction prevents the normal flow of urine from the kidney, through the ureter, and into the bladder. It can lead to hydronephrosis and impaired kidney function if not corrected.

Use this code for congenital conditions where imaging studies (e.g., ultrasound, VCUG) or surgical findings confirm an obstruction at the ureterovesical junction. This diagnosis is typically made in infants or young children presenting with urinary tract infections, palpable abdominal masses, or antenatal hydronephrosis.

• Distinguish from acquired ureteral obstructions, which are coded differently.
• Always look for documentation of laterality (e.g., left, right, bilateral) and code appropriately if specified.
• Consider sequencing with codes for associated conditions like hydronephrosis (N13.0-N13.3) or renal dysplasia (Q61.4).