Congenital occlusion of ureteropelvic junction

This code describes a birth defect where the connection between the kidney's collecting system (renal pelvis) and the ureter is narrowed or completely blocked. This obstruction prevents normal urine flow from the kidney to the bladder, leading to urine backup and potential kidney damage. It is a congenital anomaly, meaning it is present at birth.

Assign this code when documentation clearly indicates a congenital obstruction at the ureteropelvic junction (UPJ). This typically presents with hydronephrosis identified prenatally or postnatally. Supporting documentation includes imaging reports (e.g., ultrasound, CT urogram, MAG-3 renal scan) confirming UPJ obstruction.

• Differentiate from acquired UPJ obstruction, which would be coded differently.
• Ensure documentation specifies "congenital" to support this specific code.
• Code any associated hydronephrosis separately, typically as a secondary diagnosis.