Ectopic perineal testis, bilateral

This code signifies a congenital anomaly where both testes are located outside the normal scrotal sac, specifically in the perineal region. This condition is a form of cryptorchidism, characterized by the failure of testicular descent into the scrotum, with the ectopic location being the perineum.

Use this code when documentation clearly indicates bilateral ectopic testes found in the perineum. This diagnosis is typically made during physical examination in infancy or childhood. Supporting documentation would include physician notes detailing the location of both testes outside the scrotum and within the perineal area.

• Ensure documentation specifies bilateral involvement; otherwise, a unilateral code or unspecified code may be more appropriate.
• Distinguish between ectopic testis (testis descended but to an abnormal location) and undescended testis (testis arrested in its normal path of descent).
• Do not confuse with other forms of cryptorchidism (e.g., abdominal, inguinal) or retractile testes, which are typically normal variants.