Congenital malformations of lips, not elsewhere classified

This code describes various congenital structural abnormalities of the lips that are present at birth and are not specifically categorized elsewhere. These malformations can include conditions like congenital fistulas of the lips, congenital absence of the lips, or other unspecified congenital deformities affecting the lip structure. It excludes more specific conditions such as cleft lip or macrocheilia.

Use this code when documentation clearly indicates a congenital malformation of the lips that does not fit the criteria for cleft lip (Q36.-), cleft lip with cleft palate (Q37.-), macrocheilia (Q18.6), or microcheilia (Q18.7). This code is appropriate for conditions like congenital lip pits or other non-cleft related congenital lip anomalies. Documentation should specify the congenital nature and location of the malformation.

• Carefully review documentation to differentiate between congenital lip malformations and acquired conditions or those due to trauma.
• Always check the "Excludes1" notes to avoid incorrect co-coding with cleft lip, cleft lip with cleft palate, macrocheilia, or microcheilia.
• Ensure the physician's notes explicitly state "congenital" to support the use of this code.