Persistent left superior vena cava

This code describes a congenital anomaly where the left superior vena cava (SVC) fails to regress during fetal development, resulting in its persistence. This persistent vessel typically drains into the coronary sinus, bypassing the right atrium. While often asymptomatic, it can be associated with other congenital heart defects.

Use this code when documentation explicitly states the presence of a persistent left superior vena cava, identified through imaging studies such as echocardiography, CT angiography, or venography. This diagnosis is often made incidentally during workup for other cardiac conditions or during central venous catheter placement.

• Do not confuse this with a duplicated SVC, which involves two separate SVCs draining into the right atrium.
• Always review imaging reports and physician notes for definitive identification of a persistent left SVC.
• Code any associated congenital heart defects or other anomalies separately.