Congenital aneurysm of aorta

This code signifies a congenital malformation of the aorta characterized by a localized, abnormal dilation or ballooning of the arterial wall present at birth. This structural defect can occur anywhere along the aorta and may lead to complications such as rupture, dissection, or thromboembolism.

Apply this code when documentation explicitly states a congenital aneurysm of the aorta. This diagnosis is typically supported by imaging studies such as echocardiography, CT angiography, or MRI, confirming the presence and congenital origin of the aortic dilation.

• Differentiate from acquired aortic aneurysms (e.g., atherosclerotic, syphilitic) which are coded differently.
• Ensure documentation specifies "congenital" to justify using this code; otherwise, an unspecified or acquired aneurysm code may be more appropriate.
• Code any associated complications, such as rupture or dissection, in addition to this code.