Interruption of aortic arch

This code describes a severe congenital heart defect characterized by a complete discontinuity between two segments of the aortic arch. This interruption prevents normal blood flow from the left ventricle to the descending aorta, often leading to significant circulatory compromise. It is typically associated with other complex cardiac anomalies.

Assign this code for documented cases of interrupted aortic arch, a critical congenital heart disease. Documentation should clearly specify the absence of a direct connection between the ascending and descending aorta, often requiring surgical intervention shortly after birth. This diagnosis is typically made via echocardiography or other advanced imaging.

• Differentiate from coarctation of the aorta (Q25.1), which is a narrowing, not a complete break.
• Always code associated congenital heart anomalies, such as ventricular septal defect (VSD) or patent ductus arteriosus (PDA), as these frequently coexist.
• Ensure the medical record explicitly states "interruption" or "discontinuity" of the aortic arch.