HELLP syndrome, complicating the puerperium

This code represents HELLP syndrome (Hemolysis, Elevated Liver enzymes, Low Platelets) occurring during the puerperium, the period immediately following childbirth. It is a severe, life-threatening obstetric complication characterized by microangiopathic hemolytic anemia, hepatic dysfunction, and thrombocytopenia.

Use this code when a patient is diagnosed with HELLP syndrome that develops or persists after delivery, typically within the first 42 days postpartum. Documentation should clearly state the diagnosis of HELLP syndrome and specify its occurrence during the puerperal period.

• Always sequence this code after the primary reason for the encounter if the HELLP syndrome is a complication of another condition.
• Distinguish carefully between HELLP syndrome occurring during pregnancy (O14.2-) and during the puerperium.
• Ensure documentation specifies all components of HELLP syndrome (hemolysis, elevated liver enzymes, low platelets) for accurate coding.