Endometriosis of the umbilicus

This code represents the presence of endometrial tissue abnormally located at the umbilicus. This ectopic tissue responds to hormonal fluctuations, leading to cyclical pain, bleeding, or nodule formation in the umbilical region. It is a rare manifestation of extragenital endometriosis.

Use this code when documentation clearly indicates endometriosis specifically affecting the umbilicus. This diagnosis is often supported by physical examination findings of a painful umbilical nodule, imaging (e.g., ultrasound, MRI), and sometimes confirmed by biopsy. It applies to cases where the umbilical involvement is the primary or most significant site of extragenital endometriosis.

• Ensure documentation specifies "umbilicus" as the site of endometriosis, not just general abdominal wall involvement.
• Do not confuse with umbilical hernia or other umbilical lesions; the pathology must confirm endometrial tissue.
• Sequence this code as a primary diagnosis when the umbilical endometriosis is the reason for the encounter, or as a secondary diagnosis if it's a co-morbidity.