Endometriosis of cardiothoracic space

This code represents the presence of endometrial tissue outside the uterus, specifically located within the cardiothoracic space. This ectopic tissue can cause symptoms such as chest pain, dyspnea, hemoptysis, or catamenial pneumothorax, often correlating with the menstrual cycle.

Assign this code when documentation explicitly states endometriosis affecting the heart, lungs, pleura, or mediastinum. This diagnosis is typically confirmed through imaging studies, surgical exploration, or biopsy revealing endometrial glands and stroma in the cardiothoracic region.

• Ensure documentation specifies the cardiothoracic space; do not use for endometriosis in other thoracic locations without this specificity.
• Code any associated symptoms (e.g., hemoptysis, chest pain) separately.
• Consider sequencing this code as a secondary diagnosis if a more definitive primary condition (e.g., catamenial pneumothorax) is being treated.