Endometriosis of pleura

This code signifies the presence of endometrial tissue abnormally located within the pleura, the membranes lining the lungs and chest cavity. This ectopic tissue can cause symptoms such as pleuritic chest pain, dyspnea, and hemoptysis, often correlating with the menstrual cycle.

Apply this code when documentation explicitly states a diagnosis of endometriosis affecting the pleura. This typically occurs in patients with a history of endometriosis elsewhere, presenting with respiratory symptoms. Supporting documentation would include imaging findings (e.g., CT scan showing pleural nodules or effusions) and/or biopsy confirmation of endometrial implants in the pleura.

• Always confirm the specific site of endometriosis; do not use for endometriosis in other thoracic locations (e.g., lung parenchyma).
• Code any associated symptoms (e.g., hemoptysis, dyspnea, pleuritic pain) separately, if documented.
• Consider sequencing this code after a code for generalized endometriosis (N80.9) if the pleural involvement is a manifestation of a more widespread condition.