Hereditary nephropathy, NEC w dense deposit disease

This code identifies a genetic kidney disorder characterized by abnormal kidney function and the presence of dense deposits within the glomerular basement membrane. It signifies a hereditary form of nephropathy that doesn't fit into other specific categories, specifically linked with dense deposit disease (DDD), also known as C3 glomerulopathy.

Use this code when documentation explicitly states a diagnosis of hereditary nephropathy co-occurring with dense deposit disease, and no other more specific hereditary nephropathy code applies. This typically follows a kidney biopsy confirming DDD and genetic testing or family history indicating a hereditary component.

• Ensure the documentation clearly links the hereditary nephropathy with dense deposit disease.
• Do not use this code if the dense deposit disease is acquired or secondary to another condition, or if the hereditary nephropathy is specified by another ICD-10-CM code.
• Consider sequencing this code as a primary diagnosis if it is the reason for the encounter, or as a secondary diagnosis if it is a co-morbidity impacting treatment.