Hereditary nephropathy, NEC w minor glomerular abnormality

This code signifies a genetic kidney disorder characterized by impaired renal function due to structural defects in the nephrons, specifically involving minor glomerular abnormalities. It represents inherited forms of kidney disease that do not fit into more specific categories of hereditary nephropathies.

Use this code when documentation indicates a diagnosis of hereditary nephropathy with a biopsy confirming minor glomerular abnormalities, and the specific genetic cause or syndrome is not otherwise classified. This typically applies to cases where a genetic predisposition to kidney disease is identified, but a more precise ICD-10-CM code is unavailable.

• Ensure documentation specifies "hereditary" or "familial" and "minor glomerular abnormality" to support this code.
• Do not use this code if a more specific hereditary nephropathy (e.g., Alport syndrome, Fabry disease) is documented; those have their own distinct codes.
• Consider sequencing this code as a primary diagnosis when it is the reason for the encounter, or as a secondary diagnosis when it is a co-morbidity impacting patient care.