Myositis ossificans progressiva, multiple sites

This code represents fibrodysplasia ossificans progressiva (FOP), a rare genetic disorder characterized by the progressive heterotopic ossification of soft tissues, including muscles, tendons, and ligaments. This ossification leads to the formation of extra-skeletal bone, causing significant functional impairment and joint immobility across multiple anatomical sites.

Apply this code when documentation confirms a diagnosis of fibrodysplasia ossificans progressiva affecting various body regions. This diagnosis is typically established through genetic testing, characteristic clinical findings, and imaging studies demonstrating widespread heterotopic ossification.

• Ensure documentation specifies "multiple sites" to support the specificity of this code.
• Do not confuse with localized myositis ossificans (M61.0-), which is typically post-traumatic and not progressive.
• Consider sequencing this as a primary diagnosis when it is the reason for the encounter, or as a secondary diagnosis when managing complications.