Myositis ossificans progressiva, right forearm

This code signifies a rare, progressive genetic disorder characterized by the formation of bone in muscles, tendons, ligaments, and other connective tissues, specifically affecting the right forearm. This abnormal bone growth, known as heterotopic ossification, leads to severe functional impairment and restricted movement in the affected limb.

Apply this code when documentation confirms a diagnosis of myositis ossificans progressiva (also known as fibrodysplasia ossificans progressiva or FOP) with specific involvement of the right forearm. This diagnosis is typically supported by clinical examination, imaging studies (X-rays, CT scans), and often genetic testing confirming mutations in the ACVR1 gene.

• Ensure documentation clearly specifies "progressiva" to differentiate from localized or traumatic myositis ossificans.
• Verify the laterality (right forearm) is explicitly stated in the medical record.
• Consider sequencing this code as a primary diagnosis when it is the main reason for the encounter, especially for management of this specific condition.