Myositis ossificans progressiva, right upper arm

This code identifies a rare, severe genetic disorder characterized by the progressive formation of bone in muscles, tendons, ligaments, and other connective tissues, specifically affecting the right upper arm. This heterotopic ossification leads to significant functional impairment and immobility in the affected limb.

Use this code when documentation clearly indicates a diagnosis of myositis ossificans progressiva (also known as fibrodysplasia ossificans progressiva) with specific involvement of the right upper arm. This diagnosis is typically confirmed through genetic testing, imaging studies (X-rays, CT scans), and clinical presentation of progressive heterotopic ossification.

• Ensure the documentation specifies "progressiva" to differentiate from myositis ossificans traumatica.
• Verify the laterality (right upper arm) is explicitly stated in the medical record.
• Consider additional codes for associated complications, such as contractures or functional limitations.