Myositis ossificans progressiva, right shoulder

This code identifies a rare, severe genetic disorder characterized by the progressive formation of heterotopic bone in muscles, tendons, ligaments, and other connective tissues, specifically affecting the right shoulder. This ossification leads to significant pain, swelling, and progressive loss of joint mobility.

Apply this code when documentation clearly indicates a diagnosis of myositis ossificans progressiva (also known as fibrodysplasia ossificans progressiva) with specific involvement of the right shoulder. Supporting documentation should include genetic testing results, imaging studies (e.g., X-rays, CT scans) demonstrating heterotopic bone formation, and clinical notes detailing the progressive nature of the condition and its impact on the right shoulder.

• Ensure the documentation explicitly states "progressiva" or "fibrodysplasia ossificans progressiva" to differentiate from localized myositis ossificans.
• Verify laterality. This code is specific to the right shoulder; use the appropriate code for other sites or unspecified laterality.
• Consider sequencing this code as a primary diagnosis when it is the main reason for the encounter, especially for management of this specific condition.