Familial chondrocalcinosis, multiple sites

This code signifies a genetic disorder characterized by the widespread deposition of calcium pyrophosphate dihydrate (CPPD) crystals in the cartilage of multiple joints. This crystal deposition leads to inflammation, pain, and degenerative changes, often mimicking osteoarthritis. The familial aspect indicates an inherited predisposition to this condition.

Use this code when documentation explicitly states a diagnosis of familial chondrocalcinosis affecting more than one joint. This diagnosis is typically supported by imaging studies (e.g., X-rays showing chondrocalcinosis) and a family history consistent with the inherited form of the disease. It should be assigned when the systemic, multi-joint involvement is clearly documented.

• Ensure documentation specifies "familial" and "multiple sites" to accurately assign this code.
• Distinguish from acquired or idiopathic chondrocalcinosis, which would be coded differently (e.g., M11.2-).
• Code any associated arthritis (e.g., M14.4- for CPPD arthritis) as a secondary diagnosis, if documented.