Familial chondrocalcinosis, unspecified site

This code signifies a genetic disorder characterized by the deposition of calcium pyrophosphate dihydrate crystals within articular cartilage and other joint tissues, leading to recurrent episodes of acute arthritis or chronic arthropathy. It is inherited in an autosomal dominant pattern and can affect multiple joints.

Assign this code when documentation confirms a diagnosis of familial chondrocalcinosis without specifying the particular joint(s) affected. This diagnosis is typically supported by a family history of the condition, characteristic radiographic findings (chondrocalcinosis), and/or synovial fluid analysis showing calcium pyrophosphate crystals.

• Do not use this code if the specific anatomical site of chondrocalcinosis is documented; instead, use a more specific code from the M11.1- series.
• Consider sequencing this code as a primary diagnosis when it is the reason for the encounter, or as a secondary diagnosis if it is an underlying condition impacting treatment of another primary diagnosis.
• Ensure the medical record clearly distinguishes familial chondrocalcinosis from sporadic calcium pyrophosphate deposition disease (CPPD) to support accurate coding.