Felty's syndrome, multiple sites

This code identifies Felty's syndrome, a rare and severe complication of rheumatoid arthritis characterized by the triad of seropositive rheumatoid arthritis, splenomegaly, and neutropenia. The "multiple sites" designation indicates that the systemic manifestations of the syndrome are present.

Assign this code for patients diagnosed with Felty's syndrome where the clinical documentation explicitly states or implies systemic involvement beyond a single joint. This typically includes findings of splenomegaly and neutropenia in a patient with established rheumatoid arthritis. Documentation should clearly support the presence of all three components of the syndrome.

• Always code the underlying rheumatoid arthritis (e.g., M05.xx) first, as Felty's syndrome is a manifestation of rheumatoid arthritis.
• Ensure documentation specifies neutropenia and splenomegaly in addition to rheumatoid arthritis for accurate coding of Felty's syndrome.
• Do not confuse with other forms of rheumatoid arthritis without the specific triad of Felty's syndrome.