Felty's syndrome, unspecified site

This code identifies Felty's syndrome, a rare and severe complication of rheumatoid arthritis characterized by the triad of seropositive rheumatoid arthritis, splenomegaly, and neutropenia. It indicates that the specific anatomical site of involvement, if any, is not documented or is not applicable.

Use this code when documentation confirms a diagnosis of Felty's syndrome without specifying a particular affected site. This typically applies when the systemic manifestations of the syndrome (e.g., neutropenia, splenomegaly) are the primary focus, rather than a specific joint or organ. Supporting documentation would include physician notes detailing the presence of rheumatoid arthritis, splenomegaly, and neutropenia.

• Always code the underlying rheumatoid arthritis first, followed by this code for Felty's syndrome.
• Do not use this code if a specific site of Felty's syndrome involvement is documented; instead, use a more specific code if available.
• Ensure documentation clearly distinguishes Felty's syndrome from other complications of rheumatoid arthritis.