Other specified acantholytic disorders

This code represents various skin conditions characterized by acantholysis, which is the loss of cohesion between keratinocytes in the epidermis, leading to blister formation. These disorders are distinct from pemphigus (L10.-) but share the underlying pathological process of epidermal cell detachment.

Apply this code for diagnoses such as Hailey-Hailey disease (familial benign chronic pemphigus), Darier's disease (keratosis follicularis), or transient acantholytic dermatosis (Grover's disease). Documentation should clearly indicate an acantholytic disorder that is not classified under pemphigus or other more specific codes.

• Differentiate carefully from pemphigus (L10.-) based on specific diagnostic criteria and physician documentation.
• Ensure the physician's notes explicitly state an "acantholytic disorder" and provide enough detail to rule out more specific codes.
• This code is for conditions where acantholysis is a primary pathological feature, not merely a secondary finding.