Acquired keratosis follicularis

This code represents an acquired skin condition characterized by follicular papules, often with a central keratotic plug. It is a non-hereditary disorder affecting the hair follicles, leading to rough, elevated lesions that can be flesh-colored, reddish-brown, or yellowish.

Assign this code when documentation clearly indicates a diagnosis of acquired keratosis follicularis. This typically involves a dermatologist's assessment of characteristic skin lesions that developed later in life, rather than being present at birth. Supporting documentation would include clinical notes describing the appearance and distribution of the follicular papules.

• Differentiate carefully between acquired and congenital forms; the "Excludes1" note is critical.
• Ensure the physician's documentation specifies "acquired" to justify using this code.
• Do not use this code for Darier-White disease, which is a congenital form of keratosis follicularis.