Cereb autosom dom artopath w subcort infarcts & leukoenceph

This code represents Cerebral Autosomal Dominant Arteriopathy with Subcortical Infarcts and Leukoencephalopathy (CADASIL), a hereditary small vessel disease affecting the brain. It is characterized by recurrent strokes, cognitive decline, migraine with aura, and psychiatric disturbances, resulting from progressive damage to the cerebral small arteries.

Use this code when documentation clearly indicates a diagnosis of CADASIL, often confirmed by genetic testing for NOTCH3 gene mutations or characteristic MRI findings (e.g., confluent white matter hyperintensities, lacunar infarcts, temporal lobe involvement). This code is appropriate for patients presenting with symptoms consistent with CADASIL or for those undergoing follow-up for a confirmed diagnosis.

• Ensure documentation specifies "CADASIL" or explicitly describes the full condition to support this specific code.
• Do not confuse with other forms of cerebral small vessel disease without the confirmed genetic basis or characteristic clinical picture of CADASIL.
• Sequence this code as a primary diagnosis when CADASIL is the reason for the encounter, or as a secondary diagnosis when managing complications or associated conditions.