Other rheumatic aortic valve diseases

This code represents various forms of rheumatic heart disease affecting the aortic valve, excluding those specifically categorized as rheumatic aortic stenosis or insufficiency. It encompasses other structural or functional abnormalities of the aortic valve that are a sequela of rheumatic fever.

Use this code when documentation specifies a rheumatic etiology for an aortic valve disease that doesn't fit the descriptions of stenosis or insufficiency. This includes conditions like rheumatic aortic valve calcification, thickening, or other unspecified rheumatic deformities. Documentation should clearly link the aortic valve pathology to a history of rheumatic fever.

• Do not use this code for non-rheumatic aortic valve conditions; ensure the rheumatic etiology is explicitly stated.
• Consider sequencing this code after an acute rheumatic fever code (I00-I02) if the acute episode is still active and contributing to the valve disease.
• Differentiate carefully from I06.0 (rheumatic aortic stenosis) and I06.1 (rheumatic aortic insufficiency) based on the specific valve pathology documented.