Pigmentary glaucoma, unspecified eye, severe stage

This code describes a form of secondary open-angle glaucoma characterized by the dispersion of pigment from the iris, leading to its deposition in the anterior chamber and subsequent obstruction of the trabecular meshwork. This specific code indicates that the condition affects an unspecified eye and has progressed to a severe stage, implying significant optic nerve damage and visual field loss.

Use this code when documentation clearly states a diagnosis of pigmentary glaucoma with severe stage involvement, and the affected eye is not specified (e.g., "pigmentary glaucoma, severe stage"). This code is appropriate when the physician's assessment indicates advanced disease progression, often evidenced by extensive visual field defects and high intraocular pressure despite treatment.

• Ensure the documentation explicitly states "severe stage" for pigmentary glaucoma; otherwise, a different stage code may be more appropriate.
• Avoid using this code if the affected eye (right or left) is specified; instead, use the more specific codes for right (H40.131-) or left (H40.132-) eye.
• Always sequence this code after any underlying systemic conditions that may contribute to or exacerbate the glaucoma, if applicable.