Macular corneal dystrophy, bilateral

This code signifies a rare, inherited eye disorder affecting both eyes, characterized by the accumulation of abnormal deposits within the corneal stroma. These deposits lead to progressive corneal clouding, vision impairment, and often severe visual loss over time. It is a type of corneal dystrophy specifically impacting the macula of the cornea.

Apply this code when documentation confirms a diagnosis of macular corneal dystrophy affecting both eyes. This diagnosis is typically made through slit-lamp examination, corneal imaging (e.g., confocal microscopy), and genetic testing. Use this code for patients presenting with bilateral progressive vision loss and corneal opacities consistent with this specific dystrophy.

• Ensure documentation explicitly states "macular" corneal dystrophy and confirms bilateral involvement.
• Do not confuse with other corneal dystrophies (e.g., lattice, granular) which have different ICD-10-CM codes.
• Consider sequencing this code as a primary diagnosis if it is the main reason for the encounter, or as a secondary diagnosis if managing complications or related conditions.