Unspecified hereditary corneal dystrophies, bilateral

This code signifies a diagnosis of a hereditary corneal dystrophy affecting both eyes, where the specific type of dystrophy has not been identified. These are genetic disorders characterized by the accumulation of abnormal material in the cornea, leading to vision impairment.

Use this code when documentation indicates a bilateral, inherited corneal dystrophy, but the ophthalmologist has not specified the exact type (e.g., lattice, macular, granular). This code is appropriate when the genetic or specific phenotypic classification is unknown or pending further investigation.

• Ensure documentation explicitly states "bilateral" and "hereditary" or "genetic" for accurate code assignment.
• Avoid using this code if a more specific type of hereditary corneal dystrophy (e.g., H18.513 for lattice) is documented.
• Query the provider for greater specificity if possible, as more precise codes exist for various hereditary corneal dystrophies.