Search Browse Crosswalk Fees Tools Pricing

Codelle

AI-powered medical coding assistant for healthcare practices and billers.

Pricing Privacy Terms

© 2026 Codelle. All rights reserved.

CPT® copyright 2026 American Medical Association. All rights reserved. CPT is a registered trademark of the American Medical Association. Applicable FARS/DFARS restrictions apply to government use. Fee schedules, relative value units, conversion factors and/or related components are not assigned by the AMA, are not part of CPT, and the AMA is not recommending their use.

ICD-10-CM D81.81 — Biotin-dependent carboxylase d… | Codelle

ICD-10-CM/D81.8/D81.81

D81.81

ICD-10-CM

Biotin-dependent carboxylase deficiency

Clinical Notes

Inclusion Terms

Multiple carboxylase deficiency

Excludes 1 — Not coded here

biotin-dependent carboxylase deficiency due to dietary deficiency of biotin (E53.8)

Code Hierarchy

▲D81.8Other combined immunodeficiencies

D81.81(current)

Subcodes (3)

D81.810Biotinidase deficiency

D81.818Other biotin-dependent carboxylase deficiency

D81.819Biotin-dependent carboxylase deficiency, unspecified

Same Category

D81Combined immunodeficiencies D81.0Severe combined immunodeficiency with reticular dysgenesis D81.1Severe combined immunodeficiency w low T- and B-cell numbers D81.2Severe combined immunodef w low or normal B-cell numbers D81.3Adenosine deaminase [ADA] deficiency D81.30Adenosine deaminase deficiency, unspecified D81.31

Severe combined immunodef due to adenosine deaminase defic

D81.32Adenosine deaminase 2 deficiency

D81.39Other adenosine deaminase deficiency

D81.4Nezelof's syndrome

+5 more in this category