Desmoid tumor of lower extremity and pelvic girdle

This code identifies a desmoid tumor, also known as an aggressive fibromatosis, located in the lower extremity or pelvic girdle. These are rare, locally invasive, non-metastasizing soft tissue tumors that can cause significant morbidity due to their infiltrative growth pattern.

Use this code for documented cases of desmoid tumors affecting the thigh, leg, foot, hip, or pelvic region. Supporting documentation should clearly specify the diagnosis of a desmoid tumor and its anatomical location within the lower extremity or pelvic girdle, often confirmed by biopsy and imaging studies.

• Ensure the documentation explicitly states "desmoid tumor" or "aggressive fibromatosis" and specifies the lower extremity or pelvic girdle as the site.
• Do not confuse this with other benign or malignant soft tissue tumors; desmoid tumors have distinct biological behavior.
• Consider additional codes for any associated complications, such as pain (e.g., G89.1X) or functional impairment (e.g., M62.838).