Desmoid tumor of upper extremity and shoulder girdle

This code identifies a desmoid tumor, also known as aggressive fibromatosis, specifically located in the upper extremity or shoulder girdle. These are rare, non-malignant, locally aggressive soft tissue tumors that can infiltrate surrounding tissues but do not metastasize.

Use this code when documentation confirms a diagnosis of a desmoid tumor affecting the arm, forearm, hand, or any part of the shoulder girdle (e.g., clavicle, scapula, humerus head). Supporting documentation should include pathology reports confirming desmoid tumor and imaging studies detailing the tumor's location.

• Ensure the documentation specifies the upper extremity or shoulder girdle; desmoid tumors in other locations have different codes.
• Do not confuse desmoid tumors with other benign soft tissue neoplasms or malignant sarcomas; pathology is key for differentiation.
• This code is for the primary diagnosis of the desmoid tumor; additional codes may be needed for associated symptoms or complications.