Hepatosplenic T-cell lymphoma, in remission

This code signifies a rare and aggressive form of peripheral T-cell lymphoma characterized by its predilection for the liver and spleen, and its current state of remission. It typically presents with hepatosplenomegaly, cytopenias, and circulating lymphoma cells, often lacking lymphadenopathy. Remission indicates that the signs and symptoms of the disease have significantly decreased or disappeared.

Apply this code when documentation explicitly states a diagnosis of hepatosplenic T-cell lymphoma and indicates that the disease is currently in remission. This typically follows successful treatment, such as chemotherapy or stem cell transplant, and is confirmed by imaging and laboratory studies showing no active disease.

• Ensure documentation clearly specifies "in remission" to differentiate from active disease or relapse.
• Do not use this code for other types of T-cell lymphomas or for hepatosplenic T-cell lymphoma that is not in remission.
• Consider sequencing this code after any codes for complications or sequelae related to the past treatment of the lymphoma, if applicable.