Hepatosplenic T-cell lymphoma not having achieved remission

This code describes a rare, aggressive form of mature T-cell non-Hodgkin lymphoma characterized by infiltration of the liver, spleen, and bone marrow by malignant T-lymphocytes. It typically presents with hepatosplenomegaly, thrombocytopenia, and often pancytopenia, without significant lymphadenopathy. The "not having achieved remission" indicates that the disease is still active and has not responded to initial treatment or has relapsed.

Use this code for patients diagnosed with hepatosplenic T-cell lymphoma who are currently undergoing treatment, have relapsed, or whose disease has not yet achieved complete or partial remission. Documentation should clearly state the diagnosis of hepatosplenic T-cell lymphoma and indicate the current disease status as active, persistent, or relapsed, explicitly stating that remission has not been achieved.

• Do not use this code if the patient is in remission; instead, use a code indicating remission status.
• Ensure documentation specifies "hepatosplenic" to differentiate from other T-cell lymphomas.
• Always sequence this code as a primary diagnosis when it is the reason for the encounter, unless another condition is the primary focus of treatment.