Cutaneous follicle center lymphoma, spleen

This code describes a rare, indolent (slow-growing) type of non-Hodgkin lymphoma that originates from follicular center B-cells and primarily affects the skin, but has metastasized to or originated in the spleen. While typically a cutaneous lymphoma, this specific code indicates splenic involvement, signifying a more advanced or disseminated stage of the disease.

Use this code when documentation explicitly states a diagnosis of cutaneous follicle center lymphoma with confirmed involvement of the spleen. This typically requires histological confirmation of the lymphoma type and imaging or biopsy evidence of splenic lesions. It is appropriate for both primary splenic involvement of this rare subtype or metastatic disease to the spleen.

• Ensure documentation clearly specifies "cutaneous" follicle center lymphoma and confirms splenic involvement.
• Do not confuse with other types of follicular lymphoma or other cutaneous lymphomas without splenic involvement.
• Sequence this code as the primary diagnosis when the splenic involvement of the cutaneous follicle center lymphoma is the focus of the encounter.