Cutaneous follicle center lymphoma, intrathorac lymph nodes

This code describes a specific type of non-Hodgkin lymphoma, cutaneous follicle center lymphoma, when it has metastasized or originated in the lymph nodes located within the chest cavity. This is a rare presentation, as cutaneous follicle center lymphoma typically affects the skin.

Use this code when documentation confirms a diagnosis of cutaneous follicle center lymphoma with involvement of intrathoracic lymph nodes, such as mediastinal, hilar, or bronchial lymph nodes. This diagnosis is typically established through biopsy and histopathological examination of the affected lymph nodes.

• Ensure the documentation explicitly states "cutaneous follicle center lymphoma" and specifies "intrathoracic lymph nodes" to support this code.
• Do not confuse this with primary follicular lymphoma of intrathoracic lymph nodes, which would be coded differently.
• Always sequence this code as the primary diagnosis when it is the reason for the encounter, followed by any associated signs, symptoms, or complications.