Malignant neoplasm of spleen

This code signifies the presence of a primary cancerous tumor originating in the spleen. This is a rare condition where the spleen itself is the site of the malignant growth, rather than being involved secondarily by metastasis from another organ.

Apply this code when documentation explicitly states a primary malignant neoplasm of the spleen. This diagnosis is typically confirmed through biopsy and histopathological examination. Use this code when the spleen is identified as the initial site of the malignancy.

• Ensure documentation clearly specifies a primary malignant neoplasm of the spleen, not metastatic involvement.
• Review pathology reports for definitive diagnosis of splenic malignancy.
• Remember the Excludes1 notes: do not code this with Hodgkin or non-Hodgkin lymphoma, as those are distinct conditions.