Hereditary edema of legs

This diagnosis code signifies a genetic predisposition to chronic swelling, primarily affecting the lower extremities. It represents a form of primary lymphedema, often present from birth or developing in early life, characterized by persistent, non-pitting edema due to lymphatic system dysfunction.

Apply this code when documentation clearly indicates a hereditary form of lymphedema affecting the legs, such as Milroy's disease or Meige's disease. This code is appropriate for patients presenting with congenital or early-onset lower extremity edema with a family history of similar conditions, and after ruling out secondary causes of lymphedema.

• Differentiate from acquired lymphedema (e.g., post-surgical, post-radiation) which has different ICD-9-CM codes.
• Ensure documentation specifies "hereditary" or "familial" to support this specific code.
• Consider co-reporting any associated complications, such as cellulitis or lymphangitis, with appropriate infection codes.