Hereditary peripheral neuropathy

This code represents a group of inherited disorders affecting the peripheral nervous system, leading to progressive weakness, sensory loss, and muscle atrophy. These conditions are typically chronic and can manifest with varying degrees of severity and symptom presentation depending on the specific genetic mutation.

Use this code when documentation clearly indicates a diagnosis of a hereditary peripheral neuropathy, such as Charcot-Marie-Tooth disease or hereditary sensory and autonomic neuropathy. Supporting documentation should include genetic testing results, neurological examination findings, and electromyography/nerve conduction studies confirming the inherited nature of the neuropathy.

• Distinguish from acquired peripheral neuropathies, which have different ICD-9-CM codes.
• Always review the medical record for specific types of hereditary neuropathy if available, as more specific codes might exist within the ICD-9-CM hierarchy.
• Ensure the physician's documentation explicitly states "hereditary" or "inherited" to support this diagnosis.