Hereditary spastic paraplegia

This diagnosis code identifies a group of inherited neurological disorders characterized by progressive spasticity and weakness, primarily affecting the lower limbs. It results from degeneration of the longest nerve fibers in the spinal cord, leading to gait disturbances and muscle stiffness.

Assign this code when documentation confirms a diagnosis of hereditary spastic paraplegia, often supported by genetic testing, family history, and characteristic neurological findings such as hyperreflexia and extensor plantar responses. It is appropriate for both initial diagnosis and ongoing management of this chronic condition.

• Ensure documentation specifies "hereditary" to differentiate from acquired spastic paraplegias.
• Look for associated neurological symptoms that may require additional coding, such as ataxia or optic neuropathy.
• This code is often a primary diagnosis for neurological consultations and physical therapy for gait training.