Hereditary spherocytosis

This code identifies a genetic disorder characterized by defects in red blood cell membranes, leading to fragile, sphere-shaped red blood cells that are prematurely destroyed. This results in chronic hemolytic anemia, often accompanied by jaundice, splenomegaly, and gallstones.

Apply this code for patients diagnosed with hereditary spherocytosis, confirmed by laboratory findings such as increased osmotic fragility and abnormal red blood cell morphology. Documentation should clearly indicate the inherited nature of the spherocytosis.

• Differentiate from acquired spherocytosis, which has different underlying causes.
• Code any associated complications, such as aplastic crises or cholelithiasis, in addition to the primary diagnosis.
• Ensure documentation specifies "hereditary" to support the use of this specific code.