Lymphangioma, any site

This code identifies a benign lymphatic malformation characterized by dilated lymphatic channels, which can occur in various locations throughout the body. These lesions are typically congenital and result from abnormal development of the lymphatic system, leading to fluid-filled cysts or masses.

Apply this code when documentation confirms a diagnosis of lymphangioma, regardless of its anatomical location. This includes conditions like cystic hygroma, cavernous lymphangioma, or simple lymphangioma. Supporting documentation should clearly state the diagnosis of lymphangioma.

• Do not confuse with hemangioma (vascular malformation); ensure the documentation specifies lymphatic involvement.
• If the specific site of the lymphangioma is documented, consider if a more precise ICD-9-CM code exists within the 228.1 series (e.g., 228.11 for head/neck, 228.12 for trunk).
• Code any associated complications or symptoms separately, such as infection or compression of adjacent structures.