Malignant neoplasm of round ligament of uterus

This code signifies a primary cancerous tumor originating in the round ligament of the uterus. This is a rare gynecologic malignancy affecting the fibrous cord that extends from the uterus to the labia majora.

Apply this code when documentation explicitly states a malignant neoplasm of the round ligament. This diagnosis is typically confirmed through biopsy and histopathological examination.

• Differentiate from secondary or metastatic involvement; this code is for a primary malignancy.
• Ensure documentation specifies "round ligament" and not other uterine or adnexal structures.
• Review pathology reports carefully for definitive diagnosis and primary site.