Echinococcus multilocularis infection of liver

This code signifies alveolar echinococcosis, a rare parasitic infection caused by the larval stage of Echinococcus multilocularis, specifically affecting the liver. The infection typically manifests as a slow-growing, tumor-like lesion that can invade surrounding tissues.

Use this code when documentation confirms a diagnosis of alveolar echinococcosis with primary involvement of the liver. This diagnosis is often supported by imaging studies (e.g., CT, MRI) showing characteristic liver lesions, serological tests for E. multilocularis antibodies, and/or histopathological confirmation from biopsy.

• Ensure documentation clearly specifies Echinococcus multilocularis and not other Echinococcus species (e.g., E. granulosus).
• Do not confuse with cystic echinococcosis (hydatid disease), which is caused by E. granulosus and has different ICD-9-CM codes.
• Code any associated complications or manifestations (e.g., biliary obstruction, liver failure) separately.