Primary extrapulmonary coccidioidomycosis

This code represents a fungal infection caused by Coccidioides species that has spread beyond the lungs to other body sites, such as the skin, bones, joints, or central nervous system, without evidence of primary pulmonary involvement. It indicates a disseminated form of coccidioidomycosis originating outside the respiratory system.

Use this code when documentation explicitly states primary extrapulmonary coccidioidomycosis, meaning the initial site of infection is identified as outside the lungs. This applies to cases where the patient presents with symptoms and diagnostic findings (e.g., biopsy, culture) confirming coccidioidomycosis in an extrapulmonary location, and there is no indication of a primary lung infection.

• Ensure documentation clearly specifies "primary" extrapulmonary involvement to differentiate from disseminated disease secondary to a pulmonary infection.
• Do not use this code if the extrapulmonary involvement is a complication or spread from a known primary pulmonary coccidioidomycosis; instead, code the pulmonary infection and any manifestations of dissemination.
• Look for specific sites of extrapulmonary involvement (e.g., osteomyelitis, meningitis) which may require additional codes to fully describe the patient's condition.