Metopic craniosynostosis

This code identifies a congenital anomaly characterized by the premature fusion of the metopic suture, which runs from the top of the head down the middle of the forehead to the nose. This premature fusion results in a triangular-shaped forehead (trigonocephaly) and can affect brain development and facial symmetry.

Use this code for patients diagnosed with metopic craniosynostosis, whether isolated or as part of a syndrome. Documentation should clearly state the diagnosis of metopic craniosynostosis, often supported by imaging studies like CT scans confirming the fused suture.

• Differentiate from other types of craniosynostosis; ensure the documentation specifically mentions "metopic" suture involvement.
• If the craniosynostosis is part of a recognized syndrome (e.g., Muenke syndrome), code the underlying syndrome first, followed by this code.
• Ensure laterality is not applicable as the metopic suture is a single midline structure.