Congenital absence of bladder and urethra

This code signifies a rare congenital anomaly characterized by the complete absence of the urinary bladder and urethra at birth. This condition results in severe urinary tract dysfunction and is often associated with other complex malformations.

Apply this code for newborns or infants diagnosed with agenesis of both the bladder and urethra, typically identified through prenatal imaging or postnatal examination. Documentation should clearly state the complete absence of these structures, often confirmed by imaging studies such as ultrasound or MRI.

• Ensure documentation explicitly confirms the complete absence of both bladder and urethra, not just hypoplasia or malformation.
• Code any associated congenital anomalies of the genitourinary system or other body systems separately.
• This code is typically a primary diagnosis given the severity and impact on patient care.