Renal agenesis, bilateral

This code describes a congenital anomaly characterized by the complete absence of both kidneys at birth. This severe malformation results in anuria and is incompatible with life without intervention. It is often associated with Potter sequence due to oligohydramnios.

Use this code for a definitive diagnosis of bilateral renal agenesis, typically identified prenatally via ultrasound or confirmed postnatally. Documentation should clearly state the absence of both kidneys. This diagnosis is often made in cases of stillbirth or neonatal death attributed to this condition.

• Do not confuse with unilateral renal agenesis (Q60.0) or other renal hypoplasia/dysplasia codes.
• Always sequence as the principal diagnosis when it is the reason for the encounter or admission (e.g., for counseling, termination, or postnatal care related to the condition).
• Consider additional codes for associated congenital anomalies or conditions, such as Potter sequence (Q87.49).