Unicornate uterus

This code represents a congenital uterine anomaly where only one side of the Müllerian duct develops, resulting in a uterus with a single horn and a single fallopian tube. It is often associated with the absence or rudimentary development of the contralateral kidney.

Apply this code when documentation clearly indicates a diagnosis of a unicornuate uterus, typically identified during imaging studies (e.g., ultrasound, MRI, hysterosalpingogram) or surgical exploration. This anomaly can be discovered during infertility workups, recurrent pregnancy loss investigations, or incidentally during pelvic examinations.

• Ensure the documentation specifies "unicornuate uterus" and not other uterine anomalies like bicornuate or septate uterus.
• Consider coding associated anomalies, such as renal agenesis, if documented, as these are common comorbidities.
• This code is for the congenital anomaly itself; use additional codes for any related symptoms, complications (e.g., infertility, ectopic pregnancy in a rudimentary horn), or procedures.