Ovarian streak

Ovarian streak refers to the presence of a fibrous, non-functional band of tissue in the location where an ovary would typically develop. This condition is characterized by the absence of normal ovarian follicular structures and is often associated with gonadal dysgenesis or chromosomal abnormalities. It represents a rudimentary gonad that fails to develop into a mature, functional ovary.

This code is used when documentation confirms the presence of an ovarian streak, typically identified during imaging studies (e.g., ultrasound, MRI) or surgical exploration. It is commonly seen in patients with Turner syndrome, Swyer syndrome, or other forms of primary amenorrhea and infertility where gonadal development is impaired. The diagnosis is often supported by genetic testing revealing a chromosomal anomaly.

• Ensure documentation clearly distinguishes an ovarian streak from an atrophic or absent ovary, as these have different codes.
• Always sequence this code after any underlying chromosomal abnormality (e.g., Q96.x for Turner syndrome) if present and documented.
• Do not use this code for a normally developed but non-functional ovary; it specifically refers to a rudimentary, fibrous gonad.