Congenital pancreatic cyst

This code represents a rare, non-neoplastic fluid-filled sac within the pancreas that is present at birth. These cysts are typically benign and can vary in size, sometimes causing symptoms due to compression of surrounding structures or obstruction of pancreatic ducts.

Use this code when documentation explicitly states a congenital pancreatic cyst. This diagnosis is often made antenatally via ultrasound or postnatally during imaging studies for unrelated symptoms or abdominal pain. Supporting documentation should clearly indicate the congenital nature of the cyst.

• Differentiate from acquired pancreatic cysts (e.g., pseudocysts, retention cysts) which have different etiologies and codes.
• Do not use for neoplastic pancreatic cysts (e.g., serous cystadenoma, mucinous cystic neoplasm); these require specific morphology codes.
• Sequence as a primary diagnosis when the congenital pancreatic cyst is the reason for the encounter or treatment.